Table of Contents
What is exstrophy of the bladder?
Bladder exstrophy is a complex, rare disorder that occurs early on while a fetus is developing in the womb. As the bladder is developing the abdominal wall does not fully form, leaving the pubic bones separated and the bladder exposed to the outside skin surface through an opening in the lower abdominal wall.
What are the clinical features of bladder exstrophy?
The main symptom of bladder exstrophy is the bladder protruding through an opening in the belly. Bladder exstrophy can lead to other symptoms, including: Smaller-capacity bladder. Lower-than-usual belly button.
What defect is associated with exstrophy of the bladder?
Epispadias. This is the least severe form of BEEC , in which the tube to expel urine (urethra) doesn’t fully develop. Bladder exstrophy. This defect causes the bladder to form on the outside of the body.
Where is the bladder located?
pelvis
The urinary bladder is a muscular sac in the pelvis, just above and behind the pubic bone. When empty, the bladder is about the size and shape of a pear. Urine is made in the kidneys and travels down two tubes called ureters to the bladder. The bladder stores urine, allowing urination to be infrequent and controlled.
What is cloacal exstrophy?
Cloacal exstrophy is a condition where some internal organs that are normally in the lower abdomen are exposed externally. In addition, some of these organs may not have developed correctly and the lower parts of the reproductive, urinary and intestinal tracts may not be completely formed.
Is bladder exstrophy genetic?
CEB results from early abnormal development of the intra-abdominal wall and bladder during rupture of the cloacal membrane. Though the underlying cause remains still unknown, a developmental field defect with both genetic and environmental factors is likely to play a role.
How does the bladder function?
The bladder stores urine, allowing urination to be infrequent and controlled. The bladder is lined by layers of muscle tissue that stretch to hold urine. The normal capacity of the bladder is 400-600 mL. During urination, the bladder muscles squeeze, and two sphincters (valves) open to allow urine to flow out.
What is cloacal bladder?
In cloacal exstrophy, a baby’s bladder is open in the front and the inner surface is exposed on the lower surface of the abdominal wall. The exposed bladder appears as a right and left half, with the large intestine exposed and connected in the middle.
Can you live without bladder?
It can affect your body image, and you may worry about its impact on your relationships and sex life. With enough time, you should be able to do almost everything you did before. Even if you now use a urostomy bag (to collect your urine), you can go back to work, exercise, and swim.
Can a baby survive without a bladder?
Babies also ingest some of the amniotic fluid, which fills the lungs and helps them develop. When the flow of urine out of the bladder is blocked and the lungs do not develop normally, the baby may not be able to survive.
What system is the bladder in?
The urinary system
The urinary system includes the kidneys, ureters, bladder and urethra.
Where is bladder located?
The bladder is a round, bag-like organ that stores urine. It is located in the pelvic area, just below the kidneys and right behind the pelvic bone.