Table of Contents
What is a Fontan revision?
The Fontan revision improves the circulation of blood through the Fontan circuit. After the revision, a patient typically has less liver congestion, and fewer heart rhythm issues (known as heart arrhythmia) and other heart problems. The revision can also make it easier for people to be physically active.
What is a modified Fontan procedure?
Background A modification of the Fontan procedure with unidirectional cavopulmonary connection is described in which the superior vena cava (SVC) is connected to the left pulmonary artery (PA) and the inferior vena cava (IVC) is connected to the right PA via a lateral tunnel with a snare-controlled, adjustable atrial …
Can you live a long time with Fontan surgery?
Conclusions: Over 80% of patients who survive Fontan surgery will be alive at 20 years. Developing late sequelae including protein losing enteropathy, ventricular dysfunction or requiring a pacemaker predict a higher risk of late death.
How long can a Fontan last?
How long can you live with Fontan surgery?
Fontan type was atriopulmonary (AP) connection in 201 and total cavopulmonary connection (TCPC) in 482 patients. Of the TCPCs, 249 were lateral tunnels and 233 were extracardiac conduits. Survival for the entire cohort was 90% at 30 years and 80% at 40 years of life.
What was the original purpose of the Fontan procedure?
Originally designed by Fontan for treatment of tricuspid atresia, the procedure has undergone 2 major successive technical modifications. 1–3 In its first version, the atriopulmonary connection (AP), the right atrial chamber was isolated by the closure of the atrial septal defect and the hypoplastic tricuspid valve.
What are the mortality and morbidity associated with Fontan surgery?
Twenty-eight late deaths occurred a median of 7 years (1 to 11 years) after the Fontan procedure, 25 with an atriopulmonary connection, and 3 with a lateral tunnel. Two patients died of intractable protein-losing enteropathy 6 and 9 years after Fontan completion.
How many patients were excluded from the Fontan procedure study?
Thirty-three patients (14 with an atriopulmonary connection, 15 with a lateral tunnel, and 4 with an extracardiac conduit) who had been referred from foreign countries were excluded from the study of the long-term impact of the Fontan procedure.
How often do patients undergo a bidirectional Glenn before a Fontan?
Since 1990, the majority of patients (91/149 versus 1/156; P <0.001) underwent a bidirectional Glenn as a staged procedure before Fontan completion. The bidirectional Glenn was performed at a median age of 1.3 years (0.8 to 2.4 years), and the median interval time between this procedure and Fontan completion was 2.9 years (1.9 to 4 years).