What is an Askin tumor?

What is an Askin tumor?

Askin tumor is locally aggressive tumor and localized to thoracopulmonary region. It is a rare disorder mimicking common pediatric conditions such as tuberculosis, lymphoma, neuroblastoma, and rhabdomyosarcoma. So, early diagnosis and timely intervention is critical for favorable outcome of the patients.

What is the most common primary chest wall malignancy?

Chondrosarcoma. Chondrosarcomas, the most common malignant primary tumors of the chest wall, usually occur in the anterior part of the wall, arising from the costochondral arches or sternum (,26). Extraosseous chondrosarcomas are much less common. Nineteen percent of chondrosarcomas occur in the ribs.

What is chest wall metastasis?

Chest wall tumors can develop in the bones, soft tissues and cartilage of the chest cavity, which contains the heart, lungs and other organs. These tumors typically involve invasion or have metastasized from adjacent thoracic tumors, and are malignant in more than half of cases.

Are chest wall tumors cancerous?

Like all tumors, chest wall tumors may be malignant (cancerous) or benign (non-cancerous), and may originate there or have spread from elsewhere. Only about five percent of chest wall tumors are found to be cancerous. Either type of tumor may interfere with the body’s functioning.

What causes chest wall tumors?

It is unclear what causes chest wall tumors, although diet, lifestyle choices, and hereditary factors are believed to play a role. Soft-tissue chest wall tumors don’t usually cause symptoms until the tumor is advanced. Tumors that are made up of cartilage or bone often cause pain, swelling, and impaired movement.

How is chloroma diagnosed?

CT and MR scans are helpful in identifying chloromas and devising treatment plans. In patients without prior AML diagnosis, chloromas are usually misdiagnosed as several malignant masses.

Why is it called chloroma?

In 1853, King coined the term chloroma due to its greenish hue secondary to the presence of intracellular myeloperoxidase enzyme.

Are neuroendocrine tumors curable?

Many neuroendocrine tumors can be fully removed with surgery. After that, patients undergo chemotherapy to destroy any other cancer cells. Patients who have the neuroendocrine tumor completely removed may be able to consider themselves cured of this cancer.

What does a chloroma look like?

A rare type of cancer that is made up of myeloblasts (a type of immature white blood cell) and forms outside the bone marrow and blood. The tumor cells may look green when viewed under a microscope. Chloromas can occur anywhere in the body.

What is Askin’s tumor?

Askin’s tumor is a rare, primitive neuroectodermal tumor which arises from the soft tissues of the chest wall, particularly of the paravertebral region. It was first described by Askin et al in 1979.

How should Askin’s tumor be treated?

We report two cases of Askin’s tumor with a major response to polychemotherapy and surgical resection in one case. These cases show that treatment of Askin’s tumor should be multimodal, requiring discussion in multidisciplinary tumor working groups. Background

Is Ewing sarcoma the same as Ewing sarcoma of the chest?

However, recent genetic research has led to the conclusion that it is essentially the same as Ewing sarcoma, and now is part of the collective term Ewing sarcoma family of tumors, sharing similar demographics, imaging findings and prognosis 2,3. Please see Ewing sarcoma of the chest wall for more detail.